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Tetralogy of Fallot (TOF) is the most common cause of cyanotic congenital heart disease in ventricular septal defect and pulmonary stenosis physiology. TOF is associated with many syndromes, the most common being Down Syndrome, Velocardiofacial syndrome, Holt Oram Syndrome, and Poland's syndrome. VACTERL association is rare in incidence compared to the above mentioned. 1 We report a case of TOF with the VACTERL association.
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